Microbiome profiling reveals gut dysbiosis in a transgenic mouse model of Huntington's disease.

Kong G, Cao KL, Judd LM, Li S, Renoir T, Hannan AJ.

Neurobiol Dis. 2020 Feb;135:104268. doi: 10.1016/j.nbd.2018.09.001. Epub 2018 Sep 5.

SAP97-mediated rescue of NMDA receptor surface distribution in a neuronal model of Huntington's Disease.

Ambroziak W, Fourie C, Montgomery JM.

Hippocampus. 2018 Aug 1. doi: 10.1002/hipo.22995. [Epub ahead of print]

Safety and efficacy of pridopidine in patients with Huntington's disease (PRIDE-HD): a phase 2, randomised, placebo-controlled, multicentre, dose-ranging study.

Reilmann R, McGarry A, Grachev ID, Savola JM, Borowsky B, Eyal E, Gross N, Langbehn D, Schubert R, Wickenberg AT, Papapetropoulos S, Hayden M, Squitieri F, Kieburtz K, Landwehrmeyer GB; European Hunti

Lancet Neurol. 2018 Dec 14. pii: S1474-4422(18)30391-0. doi: 10.1016/S1474-4422(18)30391-0. [Epub ahead of print]

Huntington's disease leads to decrease of GABA-A tonic subunits in the D2 neostriatal pathway and their relocalization into the synaptic cleft.

Rosas-Arellano A, Tejeda-Guzmán C, Lorca-Ponce E, Palma-Tirado L, Mantellero CA, Rojas P, Missirlis F, Castro MA.

Neurobiol Dis. 2018 Feb;110:142-153. doi: 10.1016/j.nbd.2017.11.010. Epub 2017 Dec 2.

The contribution of gender differences in motor, behavioral and cognitive features to functional capacity, independence and quality of life in patients with Huntington's disease.

Zielonka D, Ren M, De Michele G, Roos RAC, Squitieri F, Bentivoglio AR, Marcinkowski JT, Landwehrmeyer GB.

Parkinsonism Relat Disord. 2018 Jan 5. pii: S1353-8020(18)30006-3. doi: 10.1016/j.parkreldis.2018.01.006. [Epub ahead of print]

Adeno-Associated Viral Vector Serotype DJ-Mediated Overexpression of N171-82Q-Mutant Huntingtin in the Striatum of Juvenile Mice Is a New Model for Huntington's Disease.

Jang M, Lee SE, Cho IH.

Front Cell Neurosci. 2018 Jun 12;12:157. doi: 10.3389/fncel.2018.00157. eCollection 2018.

Revealing Clusters of Connected Pathways through Multisource Data Integration in Huntington's disease and Spastic Ataxia.

Kakouri A, Christodoulou C, Zachariou M, Oulas A, Minadakis G, Demetriou C, Votsi C, Papanicolaou-Zamba E, Kyproula C, Spyrou G.

IEEE J Biomed Health Inform. 2018 Aug 30. doi: 10.1109/JBHI.2018.2865569. [Epub ahead of print]

Evidence of cardiac electrical remodeling in patients with Huntington disease.

Cankar K, Melik Z, Kobal J, Starc V.

Brain Behav. 2018 Aug;8(8):e01077. doi: 10.1002/brb3.1077. Epub 2018 Jul 20.

The role of the striatum in linguistic selection: Evidence from Huntington's disease and computational modeling.

Giavazzi M, Daland R, Palminteri S, Peperkamp S, Brugières P, Jacquemot C, Schramm C, Cleret de Langavant L, Bachoud-Lévi AC.

Cortex. 2018 Dec;109:189-204. doi: 10.1016/j.cortex.2018.08.031. Epub 2018 Sep 15.

FAN1 modifies Huntington's disease progression by stabilising the expanded HTT CAG repeat.

Goold R, Flower M, Moss DH, Medway C, Wood-Kaczmar A, Andre R, Farshim P, Bates GP, Holmans P, Jones L, Tabrizi SJ.

Hum Mol Genet. 2018 Oct 24. doi: 10.1093/hmg/ddy375. [Epub ahead of print]

Transcriptional regulatory networks underlying gene expression changes in Huntington's disease.

Ament SA, Pearl JR, Cantle JP, Bragg RM, Skene PJ, Coffey SR, Bergey DE, Wheeler VC, MacDonald ME, Baliga NS, Rosinski J, Hood LE, Carroll JB, Price ND.

Mol Syst Biol. 2018 Mar 26;14(3):e7435. doi: 10.15252/msb.20167435.

Agreement between clinician-rated versus patient-reported outcomes in Huntington disease.

Carlozzi NE, Boileau NR, Perlmutter JS, Chou KL, Stout JC, Paulsen JS, McCormack MK, Cella D, Nance MA, Lai JS, Dayalu P.

J Neurol. 2018 Apr 23. doi: 10.1007/s00415-018-8852-5. [Epub ahead of print]

Hydromorphone-induced chorea as an atypical presentation of opioid neurotoxicity: A case report and review of the literature.

Martin EJ, Vaughan CL, Atayee R, Hirst JM, O'Donnell K, Edmonds KP.

Palliat Med. 2018 Jul 1:269216318786861. doi: 10.1177/0269216318786861. [Epub ahead of print]

Mutant huntingtin reduction in astrocytes slows disease progression in the bachd conditional huntington's disease mouse model.

Wood TE, Barry J, Yang Z, Cepeda C, Levine MS, Gray M.

Hum Mol Genet. 2018 Oct 12. doi: 10.1093/hmg/ddy363. [Epub ahead of print]

Neurocardiovascular pathology in Premanifest and Early Stage Huntington's Disease.

Bellosta Diago E, Pérez-Pérez J, Santos Lasaosa S, Viloria Alebesque A, Martínez-Horta S, Kulisevsky J, López Del Val J.

Eur J Neurol. 2018 Mar 14. doi: 10.1111/ene.13630. [Epub ahead of print]